Neuromyelitis optica spectrum disorders (NMOSD): diagnostic criteria

Evidence-based neurology checklist on neuromyelitis optica spectrum disorders (nmosd): diagnostic criteria: Core clinical characteristics Acute longitudinally extensive transverse myelitis (LETM) Optic neuritis (ON) Acute brainstem syndrome Symptomatic narcolepsy or diencephalic syndrome: with…

Core clinical characteristics

  • Acute longitudinally extensive transverse myelitis (LETM)
  • Optic neuritis (ON)
  • Acute brainstem syndrome
  • Symptomatic narcolepsy or diencephalic syndrome: with typical MRI brain lesions
  • Systemic cerebral syndrome: with typical MRI brain lesions
  • Area postrema syndrome (APS)

Diagnostic criteria

Classification

Core clinical characteristics

Diagnostic criteria

Classification

Core clinical characteristics

Diagnostic criteria

Classification

References

  1. Wingerchuk DM, Banwell B, Bennett JL, et al; International Panel for NMO Diagnosis. International consensus diagnostic criteria for neuromyelitis optica spectrum disorders. Neurology 2015; 85:177-189. 
  2. Dellavance A, Alvarenga RR, Rodrigues SH, Kok F, de Souza AW, Andrade LE. Anti-aquaporin-4 antibodies in the context of assorted immune-mediated diseases. Eur J Neurol 2012; 19:248-252.
  3. Argyriou AA, Makris N. Neuromyelitis optica: a distinct demyelinating disease of the central nervous system. Acta Neurol Scand 2008; 128:209-217.
  4. Shosha E, Dubey D, Palace J, et al. Area postrema syndrome: frequency, criteria, and severity in AQP4-IgG-positive NMOSD. Neurology 2018; 91:e1642-e1651. 
  5. You XF, Hu HT, Ye J. Characteristics of neuromyelitis optica spectrum disorder associated with the area postrema. Zhonghua Yi Xue Za Zhi 2018; 98:668-672. 
  6. And 22 more. Subscribe to see the full list

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