Neuromyelitis optica spectrum disorder (NMOSD): area postrema syndrome (APS)
Evidence-based neurology checklist on neuromyelitis optica spectrum disorder (nmosd): area postrema syndrome (aps): Pathogenesis This is caused by dorsal medullar lesions The lesion may extend to the upper cervical cord It occurs in aquaporin-4 (AQP4) antibody positive NMOSD Epidemiological…
Pathogenesis
- This is caused by dorsal medullar lesions
- The lesion may extend to the upper cervical cord
- It occurs in aquaporin-4 (AQP4) antibody positive NMOSD
Epidemiological features
Classic clinical triad
Pathological features
Other causes of area postrema syndrome
References
- Shosha E, Dubey D, Palace J, et al. Area postrema syndrome: frequency, criteria, and severity in AQP4-IgG-positive NMOSD. Neurology 2018; 91:e1642-e1651.
- You XF, Hu HT, Ye J. Characteristics of neuromyelitis optica spectrum disorder associated with the area postrema. Zhonghua Yi Xue Za Zhi 2018; 98:668-672.
- Popescu BF, Lennon VA, Parisi JE, et al. Neuromyelitis optica unique area postrema lesions: nausea, vomiting, and pathogenic implications. Neurology 2011; 76:1229-1237.
- Camara-Lemarroy CR, Burton JM. Area postrema syndrome: a short history of a pearl in demyelinating diseases. Mult Scler 2019; 25:325-329.
- Ciron J, Sourdrille F, Biotti D, et al. Area postrema syndrome: another feature of anti-GFAP encephalomyelitis. Mult Scler 2019; doi: 10.1177/1352458518817992 (Epub ahead of print).
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