Autoimmune encephalitis: clinical features

Evidence-based neurology checklist on autoimmune encephalitis: clinical features: Potential triggers Personal history of other autoimmune disorders Family history of other autoimmune disorders Viral infections Herpes simplex virus (HSV) encephalitis TNFα inhibitors Immune-checkpoint inhibitors…

Potential triggers

  • Personal history of other autoimmune disorders
  • Family history of other autoimmune disorders
  • Viral infections
  • Herpes simplex virus (HSV) encephalitis
  • TNFα inhibitors
  • Immune-checkpoint inhibitors (ICIs)
  • Cancer

Movement disorders

Neuropsychiatric presentations

Cognitive presentations

Seizures

Criminality

Other presentations

Predictors of good outcome

Predictors of poor outcome

Residual deficits after 24 months

References

  1. Abboud H, Probasco JC, Irani S, et al. Autoimmune encephalitis: proposed best practice recommendations for diagnosis and acute management. JNNP 2021; 92:757-768.
  2. Abboud H, Probasco J, Irani SR, et al. Autoimmune encephalitis: proposed recommendations for symptomatic and long-term management. JNNP 2021; 92:897-907.
  3. Uy CE, Binks S, Irani SR. Autoimmune encephalitis: clinical spectrum and management. Pract Neurol 2021; 21:412-423. 
  4. Gövert F, Leypoldt F, Junker R, Wandinger KP, Deuschl G, Bhatia KP, Balint B. Antibody-related movement disorders - a comprehensive review of phenotype-autoantibody correlations and a guide to testing. Neurol Res Pract 2020; 2:6.
  5. Pondrelli F, Giannoccaro MP, Bisulli F, et al. Pilomotor seizures in autoimmune limbic encephalitis: description of two GAD65 antibodies- related cases and literature review. Seizure 2022; 98:71-78. 
  6. And 3 more. Subscribe to see the full list

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