Brachio-cervical inflammatory myopathy (BCIM)
Evidence-based neurology checklist on brachio-cervical inflammatory myopathy (bcim): Clinical features The mean onset age is 24-82 years It presents with progressive weakness Weakness is most prominent in the posterior cervical and upper limb muscles The lower limbs are relatively spared…
Clinical features
- The mean onset age is 24-82 years
- It presents with progressive weakness
- Weakness is most prominent in the posterior cervical and upper limb muscles
- The lower limbs are relatively spared
Differential diagnosis
Associated disorders
Associated autoantibodies
Creatinine kinase (CK)
Muscle biopsy: features
Treatment
References
- Gao AF, Saleh PA, Kassardjian CD, Vinik O, Munoz DG. Brachio-cervical inflammatory myopathy with associated scleroderma phenotype and lupus serology. Neurol Neuroimmunol Neuroinflamm 2017; 5:e410.
- Pestronk A, Kos K, Lopate G, Al-Lozi MT. Brachio-cervical inflammatory myopathies: clinical, immune, and myopathologic features. Arthritis Rheum 2006; 54:1687-1696.
- Lucchini M, Bortolani S, Monforte M, et al. Long-term follow-up and muscle imaging findings in brachio-cervical inflammatory myopathy. Neurol Neuroimmunol Neuroinflamm 2021; 8:e1016.
