Anti U1-RNP myopathy

Evidence-based neurology checklist on anti u1-rnp myopathy: Clinical phenotypes Mixed connective tissue disease (MCTD) Systemic lupus erythematosus (SLE) Clinical features Differential diagnosis Investigations

Clinical phenotypes

  • Mixed connective tissue disease (MCTD)
  • Systemic lupus erythematosus (SLE)

Clinical features

Differential diagnosis

Investigations

References

  1. Casal-Dominguez M, Pinal-Fernandez I, Corse AM, et al. Muscular and extramuscular features of myositis patients with anti-U1-RNP autoantibodies. Neurology 2019; 92:e1416-e1426.
  2. Ge Y, Yang H, Jiang W, Tian X, Lu X, Wang G. Clinical characteristics of myositis patients with isolated anti-U1 ribonucleoprotein antibody resemble immune-mediated necrotizing myopathy. Ther Adv Musculoskelet Dis 2023; 15:1759720X231181336.
  3. Dima A, Jurcut C, Baicus C. The impact of anti-U1-RNP positivity: systemic lupus erythematosus versus mixed connective tissue disease. Rheumatol Int 2018; 38:1169-1178.

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