Vasculitic myopathy

Evidence-based neurology checklist on vasculitic myopathy: Demographic features Females comprise 60% of cases The mean age at diagnosis is 63 years Classification Clinical features Investigations Treatment

Demographic features

  • Females comprise 60% of cases
  • The mean age at diagnosis is 63 years

Classification

Clinical features

Investigations

Treatment

References

  1. Pinto MV, Warrington KJ, Soontrapa P, Koster MJ, Naddaf E. Vasculitic myopathy: clinical characteristics and long-term outcomes. Neurology 2024; 103:e210141.
  2. Kimbrough BA, Naddaf E, Warrington KJ, Jimenez RE, Koster MJ. Granulomatosis with polyangiitis presenting as obstructive uropathy and vasculitic myopathy. Rheumatology (Oxford) 2023; 62:e136-e137.
  3. Koppikar S, Al-Dabie G, Jerome D, Vinik O. Eosinophilic granulomatosis with polyangiitis presenting with myositis: case based review. Rheumatol Int 2020; 40:1163-1170.
  4. Hernandez Fustes OJ, Arteaga Rodriguez C. Comment on: Focal vasculitic myositis as a primvary manifestation of Behçet's disease. Rheumatology (Oxford) 2021; 60:e264-e265.
  5. Tanomogi N, Shimojima Y, Ichikawa T, Kishida D, Sekijima Y. Vasculitic myopathy as an early manifestation of ANCA-associated vasculitis: the necessity of its differentiation from polymyalgia rheumatica. Int J Rheum Dis 2024; 27:e70019. 
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