Subacute slerosing panencephalitis (SSPE): differentials and prognosis

Evidence-based neurology checklist on subacute slerosing panencephalitis (sspe): differentials and prognosis: Differentials of progressive myoclonic epilepsy (PME) Unverricht Lundborg disease Neuronal ceroid lipofuscinosis (NCL) Lafora body disease (LBD) Myoclonic epilepsy with ragged red fibers…

Differentials of progressive myoclonic epilepsy (PME)

  • Unverricht Lundborg disease
  • Neuronal ceroid lipofuscinosis (NCL)
  • Lafora body disease (LBD)
  • Myoclonic epilepsy with ragged red fibers (MERRF)
  • Dentato-rubro-paladal-luysian atrophy (DRPLA)
  • Sialidosis
  • Juvenile GM2 gangliosidosis
  • Tay Sach’s disease

Other differentials

Clinical course

Poor prognostic features

References

  1. Tripathy K, Chawla R, Mittal K, Farmania R, Venkatesh P, Gulati S. Ophthalmic examination as a means to diagnose subacute sclerosing panencephalitis: an optical coherence tomography and ultrawide field imaging evaluation. Eye Vis (Lond) 2017;4:1. 
  2. Raut TP, Singh MK, Garg RK, Naphade PU. Subacute sclerosing panencephalitis presenting as neuromyelitis optica. BMJ Case Rep 2012; pii: bcr2012006764. 
  3. Comert S, Vitrinel A, Gursu HA, Deniz NC, Akin Y. Subacute sclerosing panencephalitis presenting as acute disseminated encephalomyelitis. Indian J Pediatr 2006; 73:1119-1121.
  4. Jakkani RK, Sureka J, Panwar S. Subacute sclerosing panencephalitis resembling Rasmussen's encephalitis on magnetic resonance imaging. Singapore Med J 2015; 56:e147-e149. 
  5. Honarmand S, Glaser CA, Chow E, et al. Subacute sclerosing panencephalitis in the differential diagnosis of encephalitis. Neurology 2004; 63:1489-1493.
  6. And 4 more. Subscribe to see the full list

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