Subacute slerosing panencephalitis (SSPE): clinical features

Evidence-based neurology checklist on subacute slerosing panencephalitis (sspe): clinical features: Risk factors Poor vaccination history Measles acquired before the age of 5 years Associated HIV infection Cerebral features Movement disorders Repetitive behaviours Vocalisations Peripheral nerve…

Risk factors

  • Poor vaccination history
  • Measles acquired before the age of 5 years
  • Associated HIV infection

Cerebral features

Movement disorders

Repetitive behaviours

Vocalisations

Peripheral nerve features

Brainstem features

Psychiatric features

Ophthalmic features

Ocular features

Adult onset cases

References

  1. Malhotra HS, Garg RK. Pearls & Oy-sters: Pisa syndrome: an unusual feature of adult-onset fulminant SSPE. Neurology 2015; 84:e12-e14. 
  2. Garg RK. Subacute sclerosing panencephalitis. J Neurol 2008; 255:1861-1871.
  3. Mekki M, Eley B, Hardie D, Wilmshurst JM. Subacute sclerosing panencephalitis: clinical phenotype, epidemiology, and preventive interventions. Dev Med Child Neurol 2019; 61:1139-1144. 
  4. Day GS, Tai P, Moharir M, Tang-Wai DF. Teaching NeuroImages: Recurrent SSPE presenting as Anton syndrome with cortical ribboning. Neurology 2015; 85:e141-e142.
  5. Tuncel D, Ozbek AE, Demirpolat G, Karabiber H. Subacute sclerosing panencephalitis with generalized seizure as a first symptom: a case report. Jpn J Infect Dis 2006; 59:317-319.
  6. And 35 more. Subscribe to see the full list

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