Subacute slerosing panencephalitis (SSPE): clinical features
Evidence-based neurology checklist on subacute slerosing panencephalitis (sspe): clinical features: Risk factors Poor vaccination history Measles acquired before the age of 5 years Associated HIV infection Cerebral features Movement disorders Repetitive behaviours Vocalisations Peripheral nerve…
Risk factors
- Poor vaccination history
- Measles acquired before the age of 5 years
- Associated HIV infection
Cerebral features
Movement disorders
Repetitive behaviours
Vocalisations
Peripheral nerve features
Brainstem features
Psychiatric features
Ophthalmic features
Ocular features
Adult onset cases
References
- Malhotra HS, Garg RK. Pearls & Oy-sters: Pisa syndrome: an unusual feature of adult-onset fulminant SSPE. Neurology 2015; 84:e12-e14.
- Garg RK. Subacute sclerosing panencephalitis. J Neurol 2008; 255:1861-1871.
- Mekki M, Eley B, Hardie D, Wilmshurst JM. Subacute sclerosing panencephalitis: clinical phenotype, epidemiology, and preventive interventions. Dev Med Child Neurol 2019; 61:1139-1144.
- Day GS, Tai P, Moharir M, Tang-Wai DF. Teaching NeuroImages: Recurrent SSPE presenting as Anton syndrome with cortical ribboning. Neurology 2015; 85:e141-e142.
- Tuncel D, Ozbek AE, Demirpolat G, Karabiber H. Subacute sclerosing panencephalitis with generalized seizure as a first symptom: a case report. Jpn J Infect Dis 2006; 59:317-319.
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