Rapidly progressive dementia

Evidence-based neurology checklist on rapidly progressive dementia: Infective causes Prion diseases Whipple’s disease Tuberculosis Neurosyphilis HIV and other viruses Cryptococcus and other fungi Septic encephalopathy Subacute sclerosing panencephalitis (SSPE) Neurodegenerative causes Autoimmune…

Infective causes

  • Prion diseases
  • Whipple’s disease
  • Tuberculosis
  • Neurosyphilis
  • HIV and other viruses
  • Cryptococcus and other fungi
  • Septic encephalopathy
  • Subacute sclerosing panencephalitis (SSPE)

Neurodegenerative causes

Autoimmune and inflammatory causes

Systemic causes

Metabolic causes

Leukodystrophies

Toxic causes

Neoplastic causes

Vascular causes

Other causes

References

  1. Geschwind MD, Shu H, Haman A, Sejvar JJ, Miller BL. Rapidly progressive dementia. Ann Neurol 2008; 64:97-108.
  2. Josephs KA, Ahlskog JE, Parisi JE, et al. Rapidly progressive neurodegenerative dementias. Arch Neurol 2009; 66:201-207.
  3. Grau-Rivera O, Gelpi E, Nos C, et al; Neurological Tissue Bank Collaborative Group. Clinicopathological Correlations and Concomitant Pathologies in Rapidly Progressive Dementia: A Brain Bank Series. Neurodegener Dis 2015; 15:350-360.
  4. Hermann P, Zerr I. Rapidly progressive dementias - aetiologies, diagnosis and management. Nat Rev Neurol 2022 (Online ahead of print).
  5. Hermann P, Zerr I. Rapidly progressive dementias - aetiologies, diagnosis and management. Nat Rev Neurol 2022; 18:363-376.
  6. And 13 more. Subscribe to see the full list

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