Primary progressive multiple sclerosis (PPMS): differentials

Evidence-based neurology checklist on primary progressive multiple sclerosis (ppms): differentials: Neurodegenerative and hereditary differentials Motor neurone disease (MND) X-linked adrenomyeloneuropathy (AMN) Leber hereditary optic neuropathy (LHON) Hereditary spastic paraparesis (HSP)…

Neurodegenerative and hereditary differentials

  • Motor neurone disease (MND)
  • X-linked adrenomyeloneuropathy (AMN)
  • Leber hereditary optic neuropathy (LHON)
  • Hereditary spastic paraparesis (HSP)
  • Spinocerebellar ataxia (SCA)

Metabolic and nutritional differentials

Infective differentials

Inflammatory and autoimmune differentials

Toxic differentials

Other differentials

References

  1. Giovannoni G. Primary progressive multiple sclerosis. ACNR 2012; 12:8-11.
  2. Thompson AJ, Polman CH, Miller DH, et al. Primary progressive multiple sclerosis. Brain 1997; 120:1085-1096.
  3. Rice CM, Cottrell D, Wilkins A, Scolding NJ. Primary progressive multiple sclerosis: progress and challenges. JNNP 2013; 84:1100-1106.

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