Paraneoplastic encephalitis (PE): clinical features

Evidence-based neurology checklist on paraneoplastic encephalitis (pe): clinical features: Sites of involvement Cerebellum Hippocampus Insular cortex Brainstem Autonomic system Spinal cord Dorsal root ganglion Clinical manifestations Limbic features Cerebellar features Brainstem features Autonomic…

Sites of involvement

  • Cerebellum
  • Hippocampus
  • Insular cortex
  • Brainstem
  • Autonomic system
  • Spinal cord
  • Dorsal root ganglion

Clinical manifestations

Limbic features

Cerebellar features

Brainstem features

Autonomic features

Diencephalic features

Other features

Viral encephalitis

Other infections

Toxic-metabolic

Cancer related

Treatment related

References

  1. Vaišvilas M, Ciano-Petersen NL, Macarena Villagrán-García MD, Muñiz-Castrillo S, Vogrig A, Honnorat J. Paraneoplastic encephalitis: clinically based approach on diagnosis and management. Postgrad Med J 2023 (Online ahead of print).
  2. Honnorat J, Antoine JC. Paraneoplastic neurological syndromes. Orphant J Rare Dis 2007; 2:22.
  3. Voltz RD, Posner JB, Dalmau J, Graus F. Paraneoplastic encephalomyelitis: an update of the effects of the anti-Hu immune response on the nervous system and tumour. JNNP 1997; 63:133-136.
  4. Malek N, Damian M. Trismus caused by paraneoplastic brainstem encephalitis. Pract Neurol 2018; 18:146-150. 
  5. Jardine DL, Krediet CP, Robinson BA. Baroreflex failure secondary to Paraneoplastic encephalomyelitis in a 17 year old woman with neuroblastoma. JNNP 2004; 75:1650-1651.
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