Locked in syndrome (LIS): clinical features

Evidence-based neurology checklist on locked in syndrome (lis): clinical features: Defining features Quadriplegia Anarthria Lower cranial nerve paralysis Other associated features Possible associated involuntary movements Possible associated impairments Usually preserved features Good prognostic…

Defining features

  • Quadriplegia
  • Anarthria
  • Lower cranial nerve paralysis

Other associated features

Possible associated involuntary movements

Possible associated impairments

Usually preserved features

Good prognostic features

Differential diagnosis

Outcome

References

  1. Smith E, Delargy M. Locked-in syndrome. BMJ 2005; 330:406-409.
  2. Schnetzer L, McCoy M, Bergmann J, Kunz A, Leis S, Trinka E. Locked-in syndrome revisited. Ther Adv Neurol Disord 2023; 16:17562864231160873.
  3. Halan T, Ortiz JF, Reddy D, Altamimi A, Ajibowo AO, Fabara SP. Locked-in syndrome: a systematic review of long-term management and prognosis. Cureus 2021; 13:e16727. 
  4. Senthilkumaran S, Balamurugan N, Karthikeyan N, Thirumalaikolundusubramanian P. Snakebite mimicking brain death: bedside clues. Indian J Crit Care Med 2021; 25:1464.

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