Immune mediated cerebellar ataxia (IMCA): classification

Evidence-based neurology checklist on immune mediated cerebellar ataxia (imca): classification: Primary autoimmune cerebellar ataxia (PACA) antibodies Anti-ARHGAP26 Anti-CARP VIII Anti-Homer-3 Anti-La Anti-MAG Anti-Nb/AP3B2 Anti-PCA2 Anti-PCA1 Anti-PKCγ Anti-Ro Anti-Septin 5 Anti-Sj/ITPR1…

Primary autoimmune cerebellar ataxia (PACA) antibodies

  • Anti-ARHGAP26
  • Anti-CARP VIII
  • Anti-Homer-3
  • Anti-La
  • Anti-MAG
  • Anti-Nb/AP3B2
  • Anti-PCA2
  • Anti-PCA1
  • Anti-PKCγ
  • Anti-Ro
  • Anti-Septin 5
  • Anti-Sj/ITPR1
  • Anti-Thyroid peroxidase
  • Anti-Thyroglobulin
  • Anti-Tr/DNER
  • Anti-VGCC
  • Anti-Zic4

Paraneoplastic cerebellar degeneration (PCD): antibodies

Non-paraneoplastic autoimmune cerebellar ataxia: antibodies

Other IMCA syndromes

Latent autoimmune cerebellar ataxia (LACA)

References

  1. Mitoma H, Manto M, Hampe CS. Immune-mediated cerebellar ataxias: practical guidelines and therapeutic challenges. Curr Neuropharmacol 2019; 17:33-58.
  2. Mitoma H, Manto M, Hampe CS. Immune-mediated cerebellar ataxias: from bench to bedside. Cerebellum Ataxias 2017; 4:16.
  3. Mitoma H, Manto M, Hadjivassiliou M. Immune-mediated cerebellar ataxias: clinical diagnosis and treatment based on immunological and physiological mechanisms J Mov Disord 2021; 14:10-28.
  4. Hadjivassiliou M, Graus F, Honnorat J, et al. Diagnostic criteria for primary autoimmune cerebellar ataxia-guidelines from an international task force on immune-mediated cerebellar ataxias. Cerebellum 2020 (Epub ahead of print).
  5. Jarius S, Wildemann B. 'Medusa-head ataxia': the expanding spectrum of Purkinje cell antibodies in autoimmune cerebellar ataxia. Part 1: Anti-mGluR1, anti-Homer-3, anti-Sj/ITPR1 and anti-CARP VIII. J Neuroinflammation 2015; 12:166. 
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