Fibromuscular dysplasia (FMD)
Evidence-based neurology checklist on fibromuscular dysplasia (fmd): Pathology This is a segmental arterial disease It is non-atheromatous and non-inflammatory It usually affects medium-sized arteries Affected arteries Risk factors Neurological features Ophthalmic features Differential diagnosis…
Pathology
- This is a segmental arterial disease
- It is non-atheromatous and non-inflammatory
- It usually affects medium-sized arteries
Affected arteries
Risk factors
Neurological features
Ophthalmic features
Differential diagnosis
Angiography
References
- Plouin PF, Perdu J, La Batide-Alanore A, Boutouyrie P, Gimenez-Roqueplo AP, Jeunemaitre X. Fibromuscular dysplasia. Orphanet J Rare Dis 2007; 2:28.
- Touzé E, Oppenheim C, Trystram D, et al. Fibromuscular dysplasia of cervical and intracranial arteries. Int J Stroke 2010; 5:296-305.
- Touzé E, Southerland AM, Boulanger M, et al. Fibromuscular dysplasia and its neurologic manifestations: a systematic review. JAMA Neurol 2018; doi: 10.1001/jamaneurol.2018.2848 (Epub ahead of print).
- Bhuriya R, Arora R, Khosla S. Fibromuscular dysplasia of the internal carotid circulation: an unusual presentation. Vasc Med 2008; 13:41-43.
- Yeo MJ, Jeon HY, Cha MJ, et al. Isolated intracranial fibromuscular dysplasia of the posterior cerebral artery. J Clin Neurosci 2017; 43:119-121.
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