Fibromuscular dysplasia (FMD)

Evidence-based neurology checklist on fibromuscular dysplasia (fmd): Pathology This is a segmental arterial disease It is non-atheromatous and non-inflammatory It usually affects medium-sized arteries Affected arteries Risk factors Neurological features Ophthalmic features Differential diagnosis…

Pathology

  • This is a segmental arterial disease
  • It is non-atheromatous and non-inflammatory
  • It usually affects medium-sized arteries

Affected arteries

Risk factors

Neurological features

Ophthalmic features

Differential diagnosis

Angiography

References

  1. Plouin PF, Perdu J, La Batide-Alanore A, Boutouyrie P, Gimenez-Roqueplo AP, Jeunemaitre X. Fibromuscular dysplasia. Orphanet J Rare Dis 2007; 2:28. 
  2. Touzé E, Oppenheim C, Trystram D, et al. Fibromuscular dysplasia of cervical and intracranial arteries. Int J Stroke 2010; 5:296-305. 
  3. Touzé E, Southerland AM, Boulanger M, et al. Fibromuscular dysplasia and its neurologic manifestations: a systematic review. JAMA Neurol 2018; doi: 10.1001/jamaneurol.2018.2848 (Epub ahead of print).
  4. Bhuriya R, Arora R, Khosla S. Fibromuscular dysplasia of the internal carotid circulation: an unusual presentation. Vasc Med 2008; 13:41-43. 
  5. Yeo MJ, Jeon HY, Cha MJ, et al. Isolated intracranial fibromuscular dysplasia of the posterior cerebral artery. J Clin Neurosci 2017; 43:119-121. 
  6. And 14 more. Subscribe to see the full list

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