Bickerstaff brainstem encephalitis (BBE): differential diagnosis

Evidence-based neurology checklist on bickerstaff brainstem encephalitis (bbe): differential diagnosis: Autoimmune differentials Guillain Barre syndrome (GBS) Miller Fisher syndrome (MFS) Acute disseminated encephalomyelitis (ADEM) Anti Ri antibody encephalitis Anti GFAP encephalitis Infective…

Autoimmune differentials

  • Guillain Barre syndrome (GBS)
  • Miller Fisher syndrome (MFS)
  • Acute disseminated encephalomyelitis (ADEM)
  • Anti Ri antibody encephalitis
  • Anti GFAP encephalitis

Infective differentials

Other differentials

Differential features of anti GQ1b positive cases

Acronyms

References

  1. Zoghaib R, Sreij A, Maalouf N, et al. Autoimmune brainstem encephalitis: an illustrative case and a review of the literature. J Clin Med 2021; 10:2970.  
  2. Cuneo GL, Grazzini I, Guadagni M, Venturini E, Bianchi A. An atypical Bickerstaff's brainstem encephalitis with involvement of spinal cord. Neuroradiol J 2016; 29:396-399.
  3. Simard C, Vogrig A, Joubert B, et al. Clinical spectrum and diagnostic pitfalls of neurologic syndromes with Ri antibodies. Neurol Neuroimmunol Neuroinflamm 2020; 7:e699.
  4. Zhao Y, Xu C, Tuo H, Liu Y, Wang J. Rhombencephalitis due to Listeria monocytogenes infection with GQ1b antibody positivity and multiple intracranial hemorrhage: a case report and literature review. J Int Med Res 2021; 49:300060521998568.
  5. Saito T, Miyai I, Matsumura T, et al. A case of Bickerstaff's brainstem encephalitis mimicking tetanus. JNNP 2000; 69:695-696.
  6. And 7 more. Subscribe to see the full list

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