Bickerstaff brainstem encephalitis (BBE): clinical features

Evidence-based neurology checklist on bickerstaff brainstem encephalitis (bbe): clinical features: Triggers Cytomegalovirus (CMV) Campylobacter jejuni Haemophilus influenza Salmonella: typhi, paratyphi A, and dublin Mycoplasma pneumoniae COVID19 Hypopituitarism Heat stroke Typical triad Brainstem…

Triggers

  • Cytomegalovirus (CMV)
  • Campylobacter jejuni
  • Haemophilus influenza
  • Salmonella: typhi, paratyphi A, and dublin
  • Mycoplasma pneumoniae
  • COVID19
  • Hypopituitarism
  • Heat stroke

Typical triad

Brainstem features

Cerebral features

Ophthalmic features

Peripheral features

Psychiatric features

Movement disorders

Other features

Overlap syndromes

Course and prognosis

References

  1. Odaka M, Yuki N, Yamada M, et al. Bickerstaff’s brainstem encephalitis: clinical features of 62 cases and a subgroup associated with Guillain–Barré syndrome. Brain 2003; 126: 2279-2290.
  2. Shahrizaila N, Yuki N. Bickerstaff brainstem encephalitis and Fisher syndrome: anti-GQ1b antibody syndrome. JNNP 2013; 84:576-583.
  3. Kanzaki A, Yabuki S, Yuki N. Bickerstaff's brainstem encephalitis associated with cytomegalovirus infection. JNNP 1995; 58:260-261.
  4. Kanzaki A, Yabuki S, Yuki N. Bickerstaff's brainstem encephalitis associated with cytomegalovirus infection. Rinsho Shinkeigaku 1994; 34:399-401.
  5. Mori M, Koga M, Yuki N, Hattori T, Kuwabara S. Bickerstaff's brainstem encephalitis after an outbreak of Campylobacter jejuni enteritis. J Neuroimmunol 2008; 196:143-146.
  6. And 45 more. Subscribe to see the full list

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