Anti LG1 VGKC autoimmune encephalitis: faciobrachial dystonic seizures

Evidence-based neurology checklist on anti lg1 vgkc autoimmune encephalitis: faciobrachial dystonic seizures: Presentation They start before the onset of encephalitis They may present as isolated epilepsy Clinical features Triggers Implications

Presentation

  • They start before the onset of encephalitis
  • They may present as isolated epilepsy

Clinical features

Triggers

Implications

References

  1. Lee R, Buckley C, Irani SR, Vincent A. Autoantibody testing in encephalopathies. Pract Neurol 2012; 12:4-13.
  2. Vincent A, Bien CG, Irani SR, Waters P. Autoantibodies associated with diseases of the CNS: new developments and future challenges. Lancet Neurol 2011; 10:759-772.
  3. Binks SNM, Klein CJ, Waters P, Pittock SJ, Irani SR. LGI1, CASPR2 and related antibodies: a molecular evolution of the phenotypes. JNNP 2017; pii: jnnp-2017-315720 (Epub ahead of print).
  4. Rodríguez Cruz PM, Pérez Sánchez JR, Alarcón Morcillo C, Velázquez Pérez JM. Alternating faciobrachial dystonic seizures in LGI1-antibody limbic encephalitis. Pract Neurol 2016; 16:387-388.
  5. Thompson J, Bi M, Murchison AG, et al; Faciobrachial Dystonic Seizures Study Group. The importance of early immunotherapy in patients with faciobrachial dystonic seizures. Brain 2018; 141:348-356. 

Related checklists

Loading...