Anti-glycine receptor syndrome: management

Evidence-based neurology checklist on anti-glycine receptor syndrome: management: Cerebrospinal fluid (CSF) analysis Protein: this is raised White cell counts: these are high Oligoclonal bands (OCBs): these are present Magnetic resonance imaging (MRI) brain Acute treatment Long-term…

Cerebrospinal fluid (CSF) analysis

  • Protein: this is raised
  • White cell counts: these are high
  • Oligoclonal bands (OCBs): these are present

Magnetic resonance imaging (MRI) brain

Acute treatment

Long-term immunosuppressive treatment

Other treatments

Acronym

References

  1. Hinson SR, Lopez-Chiriboga AS, Bower JH, et al. Glycine receptor modulating antibody predicting treatable stiff-person spectrum disorders. Neurol Neuroimmunol Neuroinflamm 2018; 5:e438.
  2. McKeon A, Martinez-Hernandez E, Lancaster E, et al. Glycine receptor autoimmune spectrum with stiff-man syndrome phenotype. JAMA Neurol 2013; 70:44-50. 
  3. Iizuka T, Tominaga N, Kaneko J. Clinical spectrum of anti-glycine receptor antibody-associated disease. Rinsho Shinkeigaku 2013; 53:1063-1066.

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