Acute disseminated encephalomyelitis (ADEM): differential diagnosis

Evidence-based neurology checklist on acute disseminated encephalomyelitis (adem): differential diagnosis: Inflammatory differentials Multiple sclerosis (MS) Neuromyelitis optica (NMO) Neurosarcoidosis Autoimmune differentials Infective differentials Metabolic differentials Malignant differentials…

Inflammatory differentials

  • Multiple sclerosis (MS)
  • Neuromyelitis optica (NMO)
  • Neurosarcoidosis

Autoimmune differentials

Infective differentials

Metabolic differentials

Malignant differentials

Other differentials

Features suggestive of MS over ADEM

Features suggestive of ADEM over MS

References

  1. Pohl D, Alper G, Van Haren K, et al. Acute disseminated encephalomyelitis: updates on an inflammatory CNS syndrome. Neurology 2016; 87(9 Suppl 2):S38-S45.
  2. Duman Ö, Yürekli VA, Gencpinar P, et al. Unusual clinical cases that mimic acute disseminated encephalomyelitis. Acta Clin Croat 2015; 54:371-377.
  3. Rodríguez-Fernández C, López-Marín L, López-Pino MÁ, Gutiérrez-Solana LG, Soto-Insuga V, Conejo-Moreno D. Analysis of a series of cases with an initial diagnosis of acute disseminated encephalomyelitis over the period 2000-2010. Rev Neurol 2013; 57:297-305.
  4. Otowa Y, Yamakawa I, Ogawa N, et al. Amoebic encephalitis mimicking acute disseminated encephalomyelitis. Pract Neurol 2021; 21:433-434.
  5. Arenson NE, Heydemann PT. Late-onset Krabbe's disease mimicking acute disseminated encephalomyelitis. Pediatr Neurol 2005; 33:208-210. 
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