Vein of Galen aneurysmal malformation (VGAM)
Evidence-based neurology checklist on vein of galen aneurysmal malformation (vgam): Anatomy This is a congenital vascular malformation It results from the persistence of the vein of Markowski This is the embryonic median prosencephalic vein It may be caused by mutations in the EPHB4 gene…
Anatomy
- This is a congenital vascular malformation
- It results from the persistence of the vein of Markowski
- This is the embryonic median prosencephalic vein
- It may be caused by mutations in the EPHB4 gene
Epidemiological features
Lasjaunias classification
Yasargil angiographic classification
Clinical presentation
Complications
Magnetic resonance imaging (MRI) features
Investigational tests
Treatment
Poor prognostic features in foetal cases
Other pineal vascular malformations
References
- Smirniotopoulos JG, Rushing EJ, Mena H. Pineal region masses: differential diagnosis. Radiographics 1992; 12:577-596.
- Moon JH, Cho WS, Kang HS, Kim JE, Lee SJ, Han MH. Vein of galen aneurysmal malformation: endovascular management of 6 cases in a single institute. J Korean Neurosurg Soc 2011; 50:191-194.
- Vivanti A, Ozanne A, Grondin C, et al. Loss of function mutations in EPHB4 are responsible for vein of Galen aneurysmal malformation. Brain 2018; 14:979-988.
- Jones BV, Ball WS, Tomsick TA, Millard J, Crone KR. Vein of Galen aneurysmal malformation: diagnosis and treatment of 13 children with extended clinical follow-up. Am J Neuroradiol 2002; 23:1717-1724.
- Chow ML, Cooke DL, Fullerton HJ, et al. Radiological and clinical features of vein of Galen malformations. J Neurointerv Surg 2015; 7:443-448.
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