Susac syndrome: clinical features

Evidence-based neurology checklist on susac syndrome: clinical features: Pathology This is a precapillary arteriolar microangiopathy There are anti-endothelial cell antibodies (AECA) in 25% of cases Demographic features Diagnostic criteria Clinical patterns Neurological features Ophthalmological…

Pathology

  • This is a precapillary arteriolar microangiopathy
  • There are anti-endothelial cell antibodies (AECA) in 25% of cases

Demographic features

Diagnostic criteria

Clinical patterns

Neurological features

Ophthalmological features

Otological features

Dermatological features

Other features

Differential diagnosis

References

  1. Susac JO, Egan RA, Rennebohm RM, Lubow M. Susac's syndrome: 1975-2005 microangiopathy/autoimmune endotheliopathy. J Neurol Sci 2007; 257:270-272.
  2. Turc G, Monnet D, Dupin N, et al. Skin involvement in Susac's syndrome. J Neurol Sci 2011; 305:152-255.
  3. Susac J, Murtagh FR, Egan A, et al. MRI findings in Susac's syndrome. Neurology 2003; 61:1783-1787.
  4. Ferretti F, Gereveni S, Colombo B, et al. Susac's syndrome as HIV-associated immune reconstitution inflammatory syndrome. AIDS Res Ther 2013; 10:22.
  5. Kleffner I, Dorr J, Ringelstein M, et al; for the European Susac Consortium (EuSaC). Diagnostic criteria for Susac syndrome. JNNP 2016; 87:1287-1295.
  6. And 14 more. Subscribe to see the full list

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