Superficial siderosis (SS): clinical features

Evidence-based neurology checklist on superficial siderosis (ss): clinical features: Classification Type 1: classical or infratentorial Type 2: secondary Pathology Demographic features Major clinical features Other clinical features Synonyms for ventral longitudinal intraspinal fluid collection

Classification

  • Type 1: classical or infratentorial
  • Type 2: secondary

Pathology

Demographic features

Major clinical features

Other clinical features

Synonyms for ventral longitudinal intraspinal fluid collection

References

  1. Fearnley JM, Stevens JM, Rudge P. Superficial siderosis of the central nervous system. Brain 1995; 128:1051-1066.
  2. Kharytaniuk N, Cowley P, Sayal P, et al. Classical infratentorial superficial siderosis of the central nervous system: pathophysiology, clinical features and management. Pract Neurol 2022 (Online ahead of print).
  3. Wilson D, Chatterjee F, Farmer SF, et al. Infratentorial superficial siderosis: Classification, diagnostic criteria, and rational investigation pathway. Ann Neurol 2016; doi: 10.1002/ana.24850 (Epub ahead of print).
  4. Kumar N. Beyond superficial siderosis: introducing "duropathies". Neurology 2012; 78:1992-1999.
  5. Kharytaniuk N, Lim EA, Chan E, Pavlou M, Werring DJ, Bamiou DE. Olfactory dysfunction is common in classical infratentorial superficial siderosis of the central nervous system. J Neurol 2022; 269:6582-6588.
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