Sporadic fatal insomnia (SFI): clinical features

Evidence-based neurology checklist on sporadic fatal insomnia (sfi): clinical features: Demographic features The mean onset age is 43 years The mean disease duration is 30 months Sleep disorders Cognitive features Clinical features Bulbar features Other features Comparison with fatal familial…

Demographic features

  • The mean onset age is 43 years
  • The mean disease duration is 30 months

Sleep disorders

Cognitive features

Clinical features

Bulbar features

Other features

Comparison with fatal familial insomnia

Synonym

References

  1. Abu-Rumeileh S, Redaelli V, Baiardi S, et al. Sporadic fatal insomnia in Europe: phenotypic features and diagnostic challenges. Ann Neurol 2018; 84:347-360.
  2. Moody KM, Schonberger LB, Maddox RA, Zou WQ, Cracco L, Cali I. Sporadic fatal insomnia in a young woman: a diagnostic challenge: case report. BMC Neurol 2011; 11:136.
  3. Mkhitarjan T, Areškevičiūtė A, Lund EL, Marner L, Hejl AM. Sporadic fatal insomnia presenting with initial symptoms of parkinsonism and abnormal dopamine transporter imaging. Mov Disord Clin Pract 2021; 9:249-251. 
  4. Tabaee Damavandi P, Dove MT, Pickersgill RW. A review of drug therapy for sporadic fatal insomnia. Prion 2017; 11:293-299. 
  5. Chen Z, Chu M, Zhang J, et al. Clinical profiles and ethnic heterogeneity of sporadic fatal insomnia. Eur J Neurol 2023; 30:813-822.
  6. And 1 more. Subscribe to see the full list

Related checklists

Loading...