Rhombencephalitis

Evidence-based neurology checklist on rhombencephalitis: Pathology This is inflammation of the brainstem and cerebellum It is confirmed on brain imaging It is associated with cerebrospinal fluid (CSF) pleocytosis >4cells/mm Viral causes Other infective causes Inflammatory causes Autoimmune causes…

Pathology

  • This is inflammation of the brainstem and cerebellum
  • It is confirmed on brain imaging
  • It is associated with cerebrospinal fluid (CSF) pleocytosis >4cells/mm

Viral causes

Other infective causes

Inflammatory causes

Autoimmune causes

Paraneoplastic causes

Other causes

Clinical features

Differential diagnosis

Magnetic resonance imaging (MRI) brain

Investigations

Treatment

Synonym

Acronyms

References

  1. Cleaver J, James R, Rice CM. Rhomboencephalitis. Pract Neurol 2020 (Online ahead of print).
  2. Jubelt B, Mihai C, Li TM, Veerapaneni P. Rhombencephalitis / brainstem encephalitis. Curr Neurol Neurosci Rep 2011; 11:543-552.
  3. Campos LG, Trindade RA, Faistauer Â, Pérez JA, Vedolin LM, Duarte JÁ. Rhombencephalitis: pictorial essay. Radiol Bras 2016; 49:329-336.
  4. Moragas M, Martínez-Yélamos S, Majós C, Fernández-Viladrich P, Rubio F, Arbizu T. Rhombencephalitis: a series of 97 patients. Medicine (Baltimore) 2011; 90:256-261.
  5. Jeanneret V, Winkel D, Risman A, Shi H, Gombolay G. Post-infectious rhombencephalitis after coronavirus-19 infection: A case report and literature review. J Neuroimmunol 2021; 357:577623.
  6. And 10 more. Subscribe to see the full list

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