Primary angiitis of the central nervous system (PACNS): clinical features
Evidence-based neurology checklist on primary angiitis of the central nervous system (pacns): clinical features: Classification Granulomatous angiitis: this affects small-sized vessels Lymphocytic PACNS Angiographically defined PACNS: this affects medium-sized vessels Mass/tumour-like lesions…
Classification
- Granulomatous angiitis: this affects small-sized vessels
- Lymphocytic PACNS
- Angiographically defined PACNS: this affects medium-sized vessels
- Mass/tumour-like lesions
- Amyloid beta related cerebral angiitis
- Haemorrhagic PACNS: this is associated with sympathomimetic drug use
- Isolated spinal cord PACNS
- Unilateral hemispheric PACNS
- Unilateral relapsing PACNS
- Isolated small vessel PACNS (svPACNS)
Risk factors
Demographic features
Headache
Stroke and transient ischaemic attacks (TIAs)
Other clinical features
Outcomes
References
- Hajj-Ali RA, Singhal AB, Benseler S, Molloy E, Calabrese LH. Primary angiitis of the CNS. Lancet Neurol 2011; 10:561-572.
- Rehman HU. Primary angiitis of the central nervous system. J R Soc Med 2000; 93:586-588.
- Binbaum J, Hellmann DB. Primary angiitis of the central nervous system. Arch Neurol 2009; 66:704-709.
- de Boysson H, Boulouis G, Dequatre N, et al; French Vasculitis Study Group. Tumor-like presentation of primary angiitis of the central nervous system. Stroke 2016; 47:2401-2404.
- Topcuoglu MA, Jha RM, George J, Frosch MP, Singhal AB. Hemorrhagic primary CNS angiitis and vasoconstrictive drug exposure. Neurol Clin Pract 2017; 7:26-34.
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