Neuromuscular respiratory dysfunction: causes

Evidence-based neurology checklist on neuromuscular respiratory dysfunction: causes: Anterior horn cell (AHC) disorders Motor neurone disease (MND) Poliomyelitis and post-polio syndrome (PPS) Spinal muscular atrophy (SMA) Kennedy disease: X-linked spinal and bulbar muscular atrophy (SBMA)…

Anterior horn cell (AHC) disorders

  • Motor neurone disease (MND)
  • Poliomyelitis and post-polio syndrome (PPS)
  • Spinal muscular atrophy (SMA)
  • Kennedy disease: X-linked spinal and bulbar muscular atrophy (SBMA)
  • Paralytic rabies

Peripheral nerve disorders

Neuromuscular junction (NMJ) disorders

Muscle diseases

Toxins

Other causes

References

  1. Ambrosino N, Carpene N, Gherardi M. Chronic respiratory care for neuromuscular diseases in adults. Eur Respir J 2009; 34:444-451.
  2. Polkey MI, Lyall RA, Moxham J, Leigh PN. Respiratory aspects of neurological disease. JNNP 1999; 66:5-15.
  3. Gilchrist JM. Overview of neuromuscular disorders affecting respiratory function. Semin Respir Crit Care Med 2002; 23:191-200.

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