Myotonic dystrophy type 2: management

Evidence-based neurology checklist on myotonic dystrophy type 2: management: Electrocardiogram (ECG) Bradycardia Atrial tachycardia, fibrillation, and flutter Ventricular arrhythmias Prolonged PR interval Prolonged QRS duration Left anterior or posterior fascicular block Abnormal Q-waves Other…

Electrocardiogram (ECG)

  • Bradycardia
  • Atrial tachycardia, fibrillation, and flutter
  • Ventricular arrhythmias
  • Prolonged PR interval
  • Prolonged QRS duration
  • Left anterior or posterior fascicular block
  • Abnormal Q-waves

Other systemic investigations

Muscle magnetic resonance imaging (MRI) muscle

Muscle magnetic resonance imaging (MRI) brain

Cardiology referral: indications

Respiratory referral: indications tests

Respiratory treatments

Cardiac treatments

Muscle pain treatments

Other treatments

Anaesthetic management

References

  1. Schoser B, Montagnese F, Bassez G, et al; Myotonic Dystrophy Foundation. Consensus-based care recommendations for adults with myotonic dystrophy type 2. Neurol Clin Pract 2019; 9:343-353.
  2. Meola G. Myotonic dystrophy type 2: the 2020 update. Acta Myol 2020; 39:222-234. 
  3. Meola G, Cardani R. Myotonic dystrophy type 2: an update on clinical aspects, genetic and pathomolecular mechanism. J Neuromuscul Dis 2015; 2(s2):S59-S71.
  4. Peric S, Maksimovic R, Banko B, et al. Magnetic resonance imaging of leg muscles in patients with myotonic dystrophies. J Neurol 2017; 264:1899-1908. 
  5. Peric S, Rakocevic-Stojanovic V, Meola G. Cerebral involvement and related aspects in myotonic dystrophy type 2. Neuromuscul Disord 2021; 31:681-694.
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