Monomelic amyotrophy: management
Evidence-based neurology checklist on monomelic amyotrophy: management: Magnetic resonance imaging (MRI) spine: features Flattening of the lower cervical cord Ischaemia of the lower cervical anterior horns Dilated and enhancing engorged posterior epidural venous plexus on flexion Anterior…
Magnetic resonance imaging (MRI) spine: features
- Flattening of the lower cervical cord
- Ischaemia of the lower cervical anterior horns
- Dilated and enhancing engorged posterior epidural venous plexus on flexion
- Anterior displacement of the dura
- Hyperintense anterior horn cells
Magnetic resonance imaging (MRI) spine: dynamic contrast
Magnetic resonance imaging (MRI) muscles
Electromyogram (EMG)
Blood tests
Treatments
Synonyms
References
- Talbot K. Monomelic amyotrophy: Hirayama’s disease. Pract Neurol 2004; 4:362-365.
- Hirayama K. Juvenile muscular atrophy of distal upper extremity (Hirayama disease). Intern Med 2000; 39:283-290.
- Sonwalkar HA, Shah RS, Khan FK, et al. Imaging features in Hirayama disease. Neurol India 2008; 56:22–26.
- Tsukita K, Sakamaki-Tsukita H. Hirayama disease: oblique amyotrophy and characteristic magnetic resonance imaging findings. QJM 2018; 111:583-584.
- Desai JA, Melanson M. Teaching neuroimages: anterior horn cell hyperintensity in Hirayama disease. Neurology 2011; 77:e73.
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