Marchiafava-Bignami disease (MBD): clinical features

Evidence-based neurology checklist on marchiafava-bignami disease (mbd): clinical features: Pathology This is demyelination and necrosis of the corpus callosum It involves the entire corpus callosum: it is just the splenium in other conditions Demographic features Risk factors Classification…

Pathology

  • This is demyelination and necrosis of the corpus callosum
  • It involves the entire corpus callosum: it is just the splenium in other conditions

Demographic features

Risk factors

Classification

Cognitive features

Bulbar features

Cortical features

Other features

References

  1. Hillbom M, Saloheimo P, Fujioka S, Wszolek ZK, Juvela S, Leone MA. Diagnosis and management of Marchiafava-Bignami disease: review of CT/MRI confirmed cases. JNNP 2014; 85:168-173.
  2. Hoshino Y, Ueno Y, Shimura H, et al. Marchiafava-Bignami disease mimics motor neuron disease: case report. BMC Neurol 2013; 13:208. 
  3. Salazar G, Fragoso M, Español G, Cuadra L. Primary degeneration of the corpus callosum (Marchiafava-Bignami disease): 2 unusual clinical presentations. Neurologia 2013; 28:587-589.
  4. Singer E, Bhatt K, Prashad A, Rudman L, Gadelmoula I, Michel G. Diagnosis and management of Marchiafava-Bignami disease, a rare neurological complication of long-term alcohol abuse. Discoveries (Craiova) 2023; 11:e168.
  5. Sehgal V, Kesav P, Modi M, Ahuja CK. Acute Marchiafava-Bignami disease presenting as reversible dementia in a chronic alcoholic. BMJ Case Rep 2013; 2013:bcr2012008286.

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