KLHL11 paraneoplastic encephalitis: clinical features

Evidence-based neurology checklist on klhl11 paraneoplastic encephalitis: clinical features: Encephalitic features Brainstem encephalitis Limbic encephalitis Cerebellar features Cerebral features Myoclonic features Other features Atypical features

Encephalitic features

  • Brainstem encephalitis
  • Limbic encephalitis

Cerebellar features

Cerebral features

Myoclonic features

Other features

Atypical features

References

  1. Dubey D, Wilson MR, Clarkson B, et al. Expanded clinical phenotype, oncological associations, and immunopathologic insights of paraneoplastic kelch-like protein-11 encephalitis. JAMA Neurol 2020; 77:1420-1429. 
  2. Mahmoud A, Dubey D, Goonetilleke A, Lee G, Elhabet S, Ahmad I, Dogar M, Jacob A. Paraneoplastic KLHL11 encephalitis presenting with progressive tinnitus, hearing loss and ataxia. Pract Neurol 2025; 25:443-447. 
  3. Chai S, Liu G, Zhang Y. Anti-kelch-like protein 11 antibody-associated encephalitis: two case reports and literature review. BMC Neurol 2025; 25:297.
  4. Jin M, Brand T, Erdag Turgeon E, et al. Clinical manifestations, tumor associations, and long-term outcomes of anti-KLHL11 encephalitis. Neurol Neuroimmunol Neuroinflamm 2026; 13:e200597. 
  5. Schwarz FK, Höftberger R, Endmayr V, et al. Vestibular and ocular motor phenotype in a case of paraneoplastic autoimmune kelch-like protein-11 encephalitis. Neurol Neuroimmunol Neuroinflamm 2026; 13:e200576. 
  6. And 2 more. Subscribe to see the full list

Related checklists

Loading...