Inflammatory myopathy: classification

Dermatomyositis related primary inflammatory myopathies

• Dermatomyositis (DM)
• Dermatomyositis with vascular pathology (DM-VP)
• Juvenile dermatomyositis
• Juvenile myositis other than dermatomyositis
• Amyopathic dermatomyositis

Other primary inflammatory myopathies

Secondary inflammatory myopathies

Acronyms

References

1. Lundberg IE, Tjärnlund A, Bottai M, et al; International Myositis Classification Criteria Project consortium, The Euromyositis register and The Juvenile Dermatomyositis Cohort Biomarker Study and Repository (JDRG) (UK and Ireland). 2017 European League Against Rheumatism/American College of Rheumatology classification criteria for adult and juvenile idiopathic inflammatory myopathies and their major subgroups. Ann Rheum Dis 2017; 76:1955-1964.
2. Mariampillai K, Granger B, Amelin D, et al. Development of a new classification system for idiopathic inflammatory myopathies based on clinical manifestations and myositis-specific autoantibodies. JAMA Neurol 2018; 75:1528-1537.
3. Selva-O'Callaghan A, Pinal-Fernandez I, Trallero-Araguás E, Milisenda JC, Grau-Junyent JM, Mammen AL. Classification and management of adult inflammatory myopathies. Lancet Neurol 2018; 17:816-828.
4. Bucelli RC, Pestronk A. Immune myopathies with perimysial pathology: Clinical and laboratory features. Neurol Neuroimmunol Neuroinflamm 2018; 5:e434.
5. Kassardjian CD, Lennon VA, Alfugham NB, Mahler M, Milone M. Clinical features and treatment outcomes of necrotizing autoimmune myopathy. JAMA Neurol 2015; 72:996-1003.
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Related checklists

• Inflammatory myopathy: medical differentials
• Inflammatory myopathy: drug-induced differentials