IgG4-related disease: management

Evidence-based neurology checklist on igg4-related disease: management: Blood tests Serum IgG4 levels are elevated Imaging Cerebrospinal fluid (CSF) analysis Histopathology Treatment Treatment of refractory cases with Rituximab

Blood tests

  • Serum IgG4 levels are elevated

Imaging

Cerebrospinal fluid (CSF) analysis

Histopathology

Treatment

Treatment of refractory cases with Rituximab

References

  1. Huijbers MG, Querol LA, Niks EH, et al. The expanding field of IgG4-mediated neurological autoimmune disorders. Eur J Neurol 2015; 22:1151-1161.
  2. Dalmau J. Name a brain protein, and an autoantibody shall be found! Neurol Neuroimmunol Neuroinflamm 2015; 2:e159.
  3. Massey J. IgG4-related hypertrophic pachymeningitis coexpressing antineutrophil cytoplasmic antibodies. Neurol Neuroimmunol Neuroinflamm. 2017; 4:e341.
  4. Baptista B, Casian A, Gunawardena H, D'Cruz D, Rice CM. Neurological Manifestations of IgG4-Related Disease. Curr Treat Options Neurol 2017; 19:14.  
  5. Taniguchi T, Hamasaki A, Okamoto M. A case of suspected lymphocytic hypophysitis and organizing pneumonia during maintenance therapy for autoimmune pancreatitis associated with autoimmune thrombocytopenia. Endocr J 2006; 53:563-566.
  6. And 5 more. Subscribe to see the full list

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