Episodic ataxia (EA): differential diagnosis

Evidence-based neurology checklist on episodic ataxia (ea): differential diagnosis: Neurological differentials Basilar migraine Familial hemiplegic migraine (FHM) Paroxysmal dyskinesia Post ictal state Spinocerebellar ataxia: especially SCA 6 Periodic vestibulo-cerebellar ataxia Metabolic…

Neurological differentials

  • Basilar migraine
  • Familial hemiplegic migraine (FHM)
  • Paroxysmal dyskinesia
  • Post ictal state
  • Spinocerebellar ataxia: especially SCA 6
  • Periodic vestibulo-cerebellar ataxia

Metabolic differentials

References

  1. Jen JC, Graves TD, Hess EJ, et al. Primary episodic ataxias: diagnosis, pathogenesis and treatment. Brain 2007; 130:2484-2493.
  2. Brazis PW, Masdeu JC, Biller J. Localization in Clinical Neurology. Lippincott Williams & Wilkins 2007. Philadelphia p372.
  3. Debray FG, Lambert M, Gagne R, et al. Pyruvate dehydrogenase deficiency presenting as intermittent isolated acute ataxia. Neuropediatrics 2008; 39:20-23.

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