Dropped head syndrome (DHS): neuromuscular causes

Evidence-based neurology checklist on dropped head syndrome (dhs): neuromuscular causes: Inflammatory myopathies Polymyositis Inclusion body myositis (IBM) Metabolic myopathies Endocrine myopathies Other myopathies Muscular dystrophies Anterior horn cell (AHC) disorders Neuromuscular junction and…

Inflammatory myopathies

  • Polymyositis
  • Inclusion body myositis (IBM)

Metabolic myopathies

Endocrine myopathies

Other myopathies

Muscular dystrophies

Anterior horn cell (AHC) disorders

Neuromuscular junction and neuropathic causes

Systemic disorders

References

  1. Umapathi T, Chaudhry V, Cornblath D, Drachman D, Griffin J, Kuncl R. Head drop and camptocormia. JNNP 2002; 73:1–7.
  2. Leung H, Hui ACG, Kay R. The dropped head. Pract Neurol 2006; 6:42-43.
  3. Gourie-Devi M, Nalini A, Sandhya S. Early or late appearance of "dropped had syndrome" in amyotrophic lateral sclerosis. JNNP 2003; 74:683-686.
  4. Alhammad RM, Naddaf E. Myopathies presenting with head drop: clinical spectrum and treatment outcomes. Neuromuscul Disord 2020; 30:128-136. 
  5. Peng Y, Zhu M, Zheng J, Zhu Y, Li X, Wei C, Hong D. Bent spine syndrome as an initial manifestation of late-onset multiple acyl-CoA dehydrogenase deficiency: a case report and literature review. BMC Neurol 2015; 15:114. 
  6. And 15 more. Subscribe to see the full list

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