Dermatomyositis: management

Evidence-based neurology checklist on dermatomyositis: management: Autoantibody tests Anti MDA5 Anti Mi-2 Anti NXP2 Anti SAE Anti TIF1 Also see Neurochecklists: “Inflammatory myopathy antibodies” Muscle enzymes Electromyogram (EMG): features Muscle biopsy Magnetic resonance imaging (MRI) muscle…

Autoantibody tests

  • Anti MDA5
  • Anti Mi-2
  • Anti NXP2
  • Anti SAE
  • Anti TIF1
  • Also see Neurochecklists: “Inflammatory myopathy antibodies”

Muscle enzymes

Electromyogram (EMG): features

Muscle biopsy

Magnetic resonance imaging (MRI) muscle

Other investigations

Treatment

References

  1. Dalakas MC. Therapeutic advances and future prospects in immune-mediated inflammatory myopathies. Ther Adv Neurol Disord 2008; 1:157-166.
  2. Mammen AL. Dermatomyositis and polymyositis: Clinical presentation, autoantibodies, and pathogenesis. Ann N Y Acad Sci 2010; 1184:134-153.
  3. Amato AA, Barohn RJ. Evaluation and treatment of inflammatory myopathies. JNNP 2009; 80:1060-1068.
  4. Selva-O'Callaghan A, Pinal-Fernandez I, Trallero-Araguás E, Milisenda JC, Grau-Junyent JM, Mammen AL. Classification and management of adult inflammatory myopathies. Lancet Neurol 2018; 17:816-828. 
  5. Susac JO, Garcia-Mullin R, Glaser JS. Ophthalmoplegia in dermatomyositis. Neurology 1973; 23:305-310.
  6. And 14 more. Subscribe to see the full list

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