CIDP associated with nodal and paranodal antibodies

Evidence-based neurology checklist on cidp associated with nodal and paranodal antibodies: Neurofascin antibodies Neurofascin 155 (NF155) Neurofascin 186 Neurofascin 140 Also see Neurochecklist: CIDP with anti-neurofascin antibodies” Contactin (CNTN1) Contactin-associated protein 1 (Caspr) Other…

Neurofascin antibodies

  • Neurofascin 155 (NF155)
  • Neurofascin 186
  • Neurofascin 140
  • Also see Neurochecklist: CIDP with anti-neurofascin antibodies”

Contactin (CNTN1)

Contactin-associated protein 1 (Caspr)

Other antibodies

Antibodies with conflicting reports: DLAT

References

  1. Kuwahara M, Suzuki H, Oka N, et al. Electron microscopic abnormality and therapeutic efficacy in chronic inflammatory demyelinating polyneuropathy with anti-neurofascin155 immunoglobulin G4 antibody. Muscle Nerve 2017; doi: 10.1002/mus.25757 (Epub ahead of print).
  2. Devaux JJ, Miura Y, Fukami Y, Inoue T, Manso C, Belghazi M, Sekiguchi K, Kokubun N, Ichikawa H, Wong AH, Yuki N. Neurofascin-155 IgG4 in chronic inflammatory demyelinating polyneuropathy. Neurology 2016; 86:800-807.
  3. Querol L, Rojas-García R, Diaz-Manera J, et al. Rituximab in treatment-resistant CIDP with antibodies against paranodal proteins. Neurol Neuroimmunol Neuroinflamm 2015; 2:e149. 
  4. Koike H, Kadoya M, Kaida KI, et al. Paranodal dissection in chronic inflammatory demyelinating polyneuropathy with anti-neurofascin-155 and anti-contactin-1 antibodies. JNNP 2017; 88:465-473.
  5. Doppler K, Appeltshauser L, Villmann C, et al. Auto-antibodies to contactin-associated protein 1 (Caspr) in two patients with painful inflammatory neuropathy. Brain 2016; 139:2617-2630.
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