Anti Ri paraneoplastic syndrome: clinical features

Evidence-based neurology checklist on anti ri paraneoplastic syndrome: clinical features: Demographic features Women account for 78% of cases It is usually associated with breast or small cell lung cancers Clinical patterns Movement disorders Other clinical features Differential diagnosis Synonym

Demographic features

  • Women account for 78% of cases
  • It is usually associated with breast or small cell lung cancers

Clinical patterns

Movement disorders

Other clinical features

Differential diagnosis

Synonym

References

  1. Simard C, Vogrig A, Joubert B, et al. Clinical spectrum and diagnostic pitfalls of neurologic syndromes with Ri antibodies. Neurol Neuroimmunol Neuroinflamm 2020; pii: e699.
  2. Mancuso M, Orsucci D, Bacci A, Caldarazzo Ienco E, Siciliano G. Anti-Ri-associated paraneoplastic cerebellar degeneration. Report of a case and revision of the literature. Arch Ital Biol 2011; 149:318-322.
  3. Weizman DA, Leong WL. Anti-Ri antibody opsoclonus-myoclonus syndrome and breast cancer: a case report and a review of the literature. J Surg Oncol 2004; 87:143-145.
  4. Wirtz PW, Sillevis Smitt PA, Hoff JI, et al. Anti-Ri antibody positive opsoclonus-myoclonus in a male patient with breast carcinoma. J Neurol 2002; 249:1710-1712.
  5. Martinaud O, Guegan-Massardier E, Iasci L, Miret N, Mihout B, Hannequin D. Anti-Ri paraneoplastic syndrome associated with ophtalmoplegia, blepharospasm and palilalia. Rev Neurol (Paris) 2005; 161:81-86.
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