Anti GABA-A autoimmune encephalitis

Evidence-based neurology checklist on anti gaba-a autoimmune encephalitis: Clinical features Cognitive impairment Altered consciousness Abnormal behaviour Frequent seizures: including refractory and status epilepticus Focal neurological deficits Opsoclonus myoclonus Associated disorders Magnetic…

Clinical features

  • Cognitive impairment
  • Altered consciousness
  • Abnormal behaviour
  • Frequent seizures: including refractory and status epilepticus
  • Focal neurological deficits
  • Opsoclonus myoclonus

Associated disorders

Magnetic resonance imaging (MRI) brain

Treatment

Prognosis

References

  1. Hacohen Y, Joseph S, Kneen R, Eunson P, Lin JP, Vincent A, Lim M. Limbic encephalitis associated with elevated antithyroid antibodies. J Child Neurol 2014; 29:769-773.
  2. Petit-Pedrol M, Armangue T, Peng X, et al. Encephalitis with refractory seizures, status epilepticus, and antibodies to the GABAA receptor: a case series, characterisation of the antigen, and analysis of the effects of antibodies. Lancet Neurol 2014; 13:276-286. 
  3. Spatola M, Petit-Pedrol M, Simabukuro MM, et al. Investigations in GABAA receptor antibody-associated encephalitis. Neurology 2017; 88:1012-1020.
  4. O'Connor K, Waters P, Komorowski L, et al. GABAA receptor autoimmunity: a multicenter experience. Neurol Neuroimmunol Neuroinflamm 2019; 6:e552. 

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