Anti-basal ganglia antibody (ABGA) syndrome

Evidence-based neurology checklist on anti-basal ganglia antibody (abga) syndrome: Causes Sydenham's chorea Post streptococcal acute demyelinating encephalomyelitis (ADEM) Encephalitis lethargica PANDAS Tourette syndrome (TS) Obsessive compulsive disorder (OCD) Infantile bilateral pallidal…

Causes

  • Sydenham's chorea
  • Post streptococcal acute demyelinating encephalomyelitis (ADEM)
  • Encephalitis lethargica
  • PANDAS
  • Tourette syndrome (TS)
  • Obsessive compulsive disorder (OCD)
  • Infantile bilateral pallidal necrosis
  • Paroxysmal dystonic choreoathetosis
  • Fixed dystonia syndrome
  • Anxiety disorders
  • Depressive disorders
  • Enuresis
  • Conduct disorder
  • Attention deficit hyperactivity disorder (ADHD)

Clinical features of adult onset ABGA

Treatment

References

  1. Martino D, Church A, Giovannoni G. Are antibasal ganglia antibodies important, and clinical useful? Pract Neurol 2007; 7:32-41.
  2. Dale RC, Church AJ, Surtees RA, et al. Encephalitis lethargica syndrome : 20 new cases and evidence of basal ganglia autoimmunity. Brain 2004; 127:21-33.
  3. Edwards MJ, Trikouli E, Martino D, et al. Anti-basal ganglia antibodies in patients with atypical dystonia and tics: a prospective study. Neurology 2004; 63:156-158.
  4. Edwards MJ, Dale RC, Church AJ, Giovannoni G, Bhatia KP. A dystonic syndrome associated with anti-basal ganglia antibodies. JNNP 2004; 75:914-916.
  5. Nicholson TR, Ferdinando S, Krishnaiah RB, et al. Prevalence of anti-basal ganglia antibodies in adult obsessive-compulsive disorder: cross-sectional study. Br J Psychiatry 2012; 200:381-386.

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