ANCA associated vasculitis (AAV): classification

Evidence-based neurology checklist on anca associated vasculitis (aav): classification: Primary types Granulomatosis with polyangiitis (GPA): formerly Wegener’s granulomatosis Eosinophilic granulomatosis with polyangiitis (EGPA): formerly Churg Strauss syndrome Microscopic polyangiitis (MPA)…

Primary types

  • Granulomatosis with polyangiitis (GPA): formerly Wegener’s granulomatosis
  • Eosinophilic granulomatosis with polyangiitis (EGPA): formerly Churg Strauss syndrome
  • Microscopic polyangiitis (MPA)
  • Renal-limited vasculitis

Secondary types

Acronym

References

  1. Chung SA, Seo P. Microscopic polyangiitis. Rheum Dis Clin North Am 2010; 36:545-558.
  2. Arman F, Barsoum M, Selamet U, et al. Antineutrophil cytoplasmic antibody-associated vasculitis, update on molecular pathogenesis, diagnosis, and treatment. Int J Nephrol Renovasc Dis 2018; 11:313-319.
  3. Nishimura Y, Tsuda T, Nishina S, Omoto A, Misawa M, Yabe H, Nagao T. Silicosis, then microscopic polyangiitis-antineutrophil cytoplasmic antibodies-associated vasculitis may be work-related disease in patients with silicosis. J Gen Fam Med 2017; 18:288-290.
  4. Bartůnková J, Pelclová D, Fenclová Z, et al. Exposure to silica and risk of ANCA-associated vasculitis. Am J Ind Med 2006; 49:569-576.
  5. Beaudreuil S, Lasfargues G, Lauériere L, et al. Occupational exposure in ANCA-positive patients: a case-control study. Kidney Int 2005; 67:1961-1966.
  6. And 7 more. Subscribe to see the full list

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